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A case of Henoch Schönlein Purpura with serious multisystem involvement [J Behcet Uz Child Hosp]
J Behcet Uz Child Hosp. 2011; 1(1): 33-36 | DOI: 10.5222/buchd.2011.033  

A case of Henoch Schönlein Purpura with serious multisystem involvement

Fatma Kaya Kılıç, Özlem İnce Bağ, Demet Can, Serdar Altınöz, Aysel Öztürk
Clinic Of Pediatrics, Dr.behcet Uz Children

Henoch Schönlein Purpura (HSP) is the most frequent vasculite symdrome of childhood period. Altough it has a benign nature, it may be seen with different system involvement and may have an atypical clinical presentation. Here we present an atypical case of HSP with multi-system involvement, and not responding to coticosteroid treatment. During follow-up Familial Mediterranean Fever mutation was aslo found to be positive.

Keywords: Henoch Schönlein Purpura, Familial Mediterranean Fever


Ciddi multisistemik tutulum ile seyreden Henoch Schönlein Purpura olgusu

Fatma Kaya Kılıç, Özlem İnce Bağ, Demet Can, Serdar Altınöz, Aysel Öztürk
Dr. Behçet Uz Çocuk Hastanesi, Büyük Çocuk Servisi

Henoch Schönlein Purpurası (HSP) çocukluk çağında en sık görülen vaskülitik sendromdur. Benign seyirli olmasına rağmen farklı sistem tutulumları ile karşımıza gelebilir, atipik klinik prezentasyon gösterebilir. Multisistem tutulumu ve kortikosteroid tedavisine yanıt vermemesi nedeniyle atipik klinik seyir gösterdiği düşünülen ve izlemde Ailesel Akdeniz Ateşi (FMF) mutasyonu pozitif bulunan bir HSP olgusu sunulmuştur

Anahtar Kelimeler: Henoch Schönlein Purpurası, Ailesel Akdeniz Ateşi


Fatma Kaya Kılıç, Özlem İnce Bağ, Demet Can, Serdar Altınöz, Aysel Öztürk. A case of Henoch Schönlein Purpura with serious multisystem involvement. J Behcet Uz Child Hosp. 2011; 1(1): 33-36

Corresponding Author: Fatma Kaya Kılıç, Türkiye


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