Abstract

Infantile hepatic hemangioendotheliomas are the most common benign hepatic vascular tumors of infancy. The risk is 3 times higher in girls than boys. The diagnosis are established 75 % of cases in three months age. It is characterized by hepatomegaly, heart failure and giant hemangiomas. It can cause Kasabach-Merritt syndome like other giant hemangiomas.

İn the newborn and early infancy, Kasabach-Merritt syndrome rarely leads to prolonged jaundice as a result of shunt hyperbilirubinemia. Giant hemangiomas enlarge rapidly and lead to life threatening thrombocytopenia, microangiopathic hemolytic anemia and consumption coagulopathy.

Treatment of this syndrome includes management of thrombocytopenia, anemia and consumption coagulopathy. Surgical excision can be applied to small lesions. Mortality rate is high.

In this article we presented a case who was diagnosed as infantile hepatic hemangio endothelioma with the findings of Kasbach-Merrit syndrome, during the examination of prolonged jaundice.