Abstract

Esophageal atresia, is a congenital anomaly that is seen 1 in 2500 births and can be treated surgically. Patients can be fed orally after the anomaly is surgically corrected. Complications due to the surgery should be ruled out in cases where the patient's general condition becomes worse after being fed. If the patient's situation does not get better after doing so, existence of metabolical disorders should be considered. Methylmalonic acidemia has been detected in further investigations of a patient who was operated for esophageal atresia in our clinics as a newborn, and developed metabolical acidosis after being fed postoperatively. Although prognosis is expected to be good after the early diagnosis and treatment of organic acidemias as methylmalonic acidemia, the diagnosis might be delayed as it is a rare condition that is not first come to mind, which might result in disabilities in some cases. Our case report is the first case in the literature, as the literature scan we had made showed no previous report on correlation of esophageal atresia and organic acidemias.