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Exercise induced a rare cardiac arrest: A case with catecholaminergic polymorphic ventricular tachycardia [J Behcet Uz Child Hosp]
J Behcet Uz Child Hosp. 2017; 7(1): 65-68 | DOI: 10.5222/buchd.2017.065  

Exercise induced a rare cardiac arrest: A case with catecholaminergic polymorphic ventricular tachycardia

Şevket Ballı, Eviç Zeynep Akgün, İlker Kemal Yücel, Mustafa Orhan Bulut, Gökmen Akgün, Emine Hekim Yılmaz, Taliha Öner, Ahmet Çelebi
1Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Training & Research Hospital, Department of Pediatric Cardiology,

In this report, we present 15 years old girl with catecholaminergic polymorphic ventricular tachycardia who had cardiac resuscitation due to cardiac arrest and her sister was died from cardiac arrest. Catecholaminergic polymorphic ventricular tachycardias (CPVT), without structural cardiac abnormalities, can lead to sudden cardiac arrest during exercise or acute emotion. Patient with CPVT usually present with exercise induced syncope and diagnosis made based on family history. Background of these case highlighted the diagnosis and treatment of CPVT.

Keywords: Cathecolamin, syncope, polymorphic ventricular tachycardia


Efora Bağlı Nadir Bir Kardiak Arrest: Katekolaminerjik Polimorfik ventriküler Taşikardili Bir Olgu

Şevket Ballı, Eviç Zeynep Akgün, İlker Kemal Yücel, Mustafa Orhan Bulut, Gökmen Akgün, Emine Hekim Yılmaz, Taliha Öner, Ahmet Çelebi
Dr. Siyami Ersek Göğüs Kalp ve Damar Cerrahisi Eğitim ve Araştırma Hastanesi, Pediatrik Kardiyoloji

Biz burada 15 yaşında katekolaminerjik polimorfik ventriküler taşikardiye ( KPVT) bağlı kardiyak arrest nedeniyle resüsitasyon yapılmış, kardeşi efor esnasında kardiyak arrest nedeniyle ex olmuş bir vakayı sunduk. KPVT de hastaların kardiyak yapısal bir bozukluğu olmamasına rağmen egzersiz yada efor esnasında kardiyak arreste neden olabilmektedir. KPVT li hastalarda efor esnasında senkop ve aile hikayesi tanıda önemlidir. Biz burada KPVT li hastaların tanı ve tedavisini vurgulamak istedik.

Anahtar Kelimeler: Katekolamin, senkop, polimorfik ventriküler taşikardi


Şevket Ballı, Eviç Zeynep Akgün, İlker Kemal Yücel, Mustafa Orhan Bulut, Gökmen Akgün, Emine Hekim Yılmaz, Taliha Öner, Ahmet Çelebi. Exercise induced a rare cardiac arrest: A case with catecholaminergic polymorphic ventricular tachycardia. J Behcet Uz Child Hosp. 2017; 7(1): 65-68

Corresponding Author: Şevket Ballı, Türkiye


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